An unusual tuberous sclerosis case presenting with fibrillary astrocytoma

Eren S., Polat P., Erman Z.

PEDIATRIC NEUROSURGERY, cilt.37, sa.3, ss.118-121, 2002 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 37 Sayı: 3
  • Basım Tarihi: 2002
  • Doi Numarası: 10.1159/000064397
  • Dergi Adı: PEDIATRIC NEUROSURGERY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.118-121
  • Atatürk Üniversitesi Adresli: Evet

Özet

Tuberous sclerosis (TS) is an autosomal dominant disorder. It is characterized by hamartomatous lesions in various organs such as the brain, skin, kidneys and heart. Subependymal and parenchymal nodules occur in the cerebrum. Although giant cell astrocytoma may develop from these subependymal nodules, tumor formation is very rare in the cortical nodules. We present the clinical, computed tomography and magnetic resonance imaging findings of a fibrillary astrocytoma originating from a cortical tuber in a 4-year-old female with TS. Copyright (C) 2002 S. Karger AG, Basel.